a case series report of iranian children hemophagocytic lymphohistiocytosis syndrome

نویسندگان

roxana m. ghanaie 1 pediatric infections research center, shahid beheshti university of medical sciences, tehran, ir iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences)

reza shiari department of pediatrics, division of pediatric rheumatology, mofid children hospital, shahid beheshti university of medical sciences, ir iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences)

abdollah karimi 1 pediatric infections research center, shahid beheshti university of medical sciences, tehran, ir iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences)

shahnaz armin 1 pediatric infections research center, shahid beheshti university of medical sciences, tehran, ir iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences)

چکیده

hemophagocytic lymphohistiocytosis (hlh) is an aggressive and potentially life-threatening disease and has to be considered in the differential diagnosis of many conditions. hlh comprises two different conditions that are difficult to differentiate; familial hemophagocytic lymphohistiocytosis (fhlh) or familial erythrophagocytic lymphohistiocytosis (fel), and secondary hemophagocytic syndromes (secondary hlh, shlh). herein, we report a case series of iranian children with hlh and describe the symptoms and outcome of this disease in iran.

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عنوان ژورنال:
archives of pediatric infectious diseases

جلد ۱، شماره ۱، صفحات ۳۱-۳۵

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